Exact Mass: 189.1165
Exact Mass Matches: 189.1165
Found 131 metabolites which its exact mass value is equals to given mass value 189.1165,
within given mass tolerance error 0.01 dalton. Try search metabolite list with more accurate mass tolerance error
0.001 dalton.
Homocitrulline
Homocitrulline is a metabolite that can be detected in larger amounts in the urine of individuals with urea cycle disorders (OMIM 238970). The accumulation of carbamylphosphate due to depleted supply of ornithine for the urea cycle may be responsible for the enhanced synthesis of homocitrulline and homoarginine in some cases (PMID 2474087). Homocitrulline has been identified in the human placenta (PMID: 32033212). Homocitrulline is a metabolite that can be detected in larger amounts in the urine of individuals with urea cycle disorders (OMIM 238970). The accumulation of carbamylphosphate due to depleted supply of ornithine for the urea cycle may be responsible for the enhanced synthesis of homocitrulline and homoarginine in some cases (PMID 2474087). [HMDB] L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI). L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).
2-amino-5-[[amino(hydrazinyl)methylidene]amino]pentanoic acid
L-Homocitrulline
A L-lysine derivative that is L-lysine having a carbamoyl group at the N(6)-position. It is found in individuals with urea cycle disorders. L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI). L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).
Homocitrulline
L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI). L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).
7,9-Dimethyl-3,4-dihydro-1H-benzo[b]azepin-5(2H)-one
b-Alanine,N-(3-hydrazino-3-oxopropyl)-, hydrazide (9CI)
Ethanone,1-(5,6,7,8-tetrahydro-2-naphthalenyl)-, oxime
1-ETHYL-1,2,3,4-TETRAHYDRO-QUINOLINE-6-CARBALDEHYDE
tert-Butyl (N-hydroxycarbamimidoylmethyl)carbamate
Quinoline,1-acetyl-1,2,3,4-tetrahydro-4-methyl- (9CI)
Oxazole,4,5-dihydro-4,4-dimethyl-2-(phenylmethyl)-
1-Methyl-4-phenyl-1,2,3,6-tetrahydropyridine N-oxide
L-homocitrulline zwitterion
An amino acid zwitterion of L-homocitrulline arising from transfer of a proton from the carboxy to the amino group; major species at pH 7.3.
