[(3-Methylbutyl)amino]acetic acid (BioDeep_00000842751)
代谢物信息卡片
化学式: C7H15NO2 (145.1103)
中文名称:
谱图信息:
最多检出来源 () 0%
分子结构信息
SMILES: CC(C)CCNCC(=O)O
InChI: InChI=1S/C7H15NO2/c1-6(2)3-4-8-5-7(9)10/h6,8H,3-5H2,1-2H3,(H,9,10)
相关代谢途径
Reactome(0)
BioCyc(0)
PlantCyc(0)
代谢反应
0 个相关的代谢反应过程信息。
Reactome(0)
BioCyc(0)
WikiPathways(0)
Plant Reactome(0)
INOH(0)
PlantCyc(0)
COVID-19 Disease Map(0)
PathBank(0)
PharmGKB(0)
0 个相关的物种来源信息
在这里通过桑基图来展示出与当前的这个代谢物在我们的BioDeep知识库中具有相关联信息的其他代谢物。在这里进行关联的信息来源主要有:
- PubMed: 来源于PubMed文献库中的文献信息,我们通过自然语言数据挖掘得到的在同一篇文献中被同时提及的相关代谢物列表,这个列表按照代谢物同时出现的文献数量降序排序,取前10个代谢物作为相关研究中关联性很高的代谢物集合展示在桑基图中。
- NCBI Taxonomy: 通过文献数据挖掘,得到的代谢物物种来源信息关联。这个关联信息同样按照出现的次数降序排序,取前10个代谢物作为高关联度的代谢物集合展示在桑吉图上。
- Chemical Taxonomy: 在物质分类上处于同一个分类集合中的其他代谢物
- Chemical Reaction: 在化学反应过程中,存在为当前代谢物相关联的生化反应过程中的反应底物或者反应产物的关联代谢物信息。
点击图上的相关代谢物的名称,可以跳转到相关代谢物的信息页面。
亚细胞结构定位 | 关联基因列表 |
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文献列表
- Yan Chen, Leila R Zelnick, Matthew P Huber, Ke Wang, Nisha Bansal, Andrew N Hoofnagle, Rajan K Paranji, Susan R Heckbert, Noel S Weiss, Alan S Go, Chi-Yuan Hsu, Harold I Feldman, Sushrut S Waikar, Rupal C Mehta, Anand Srivastava, Stephen L Seliger, James P Lash, Anna C Porter, Dominic S Raj, Bryan R Kestenbaum. Association Between Kidney Clearance of Secretory Solutes and Cardiovascular Events: The Chronic Renal Insufficiency Cohort (CRIC) Study.
American journal of kidney diseases : the official journal of the National Kidney Foundation.
2021 08; 78(2):226-235.e1. doi:
10.1053/j.ajkd.2020.12.005
. [PMID: 33421453] - María L Couce, Luís Aldamiz-Echevarría, María A Bueno, Patricia Barros, Amaya Belanger-Quintana, Javier Blasco, María-Teresa García-Silva, Ana M Márquez-Armenteros, Isidro Vitoria, Inmaculada Vives, Rosa Navarrete, Ana Fernández-Marmiesse, Belén Pérez, Celia Pérez-Cerdá. Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
Journal of human genetics.
2017 Mar; 62(3):355-360. doi:
10.1038/jhg.2016.144
. [PMID: 27904153] - Yosuke Shigematsu, Ikue Hata, Go Tajima. Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.
Journal of inherited metabolic disease.
2010 Oct; 33(Suppl 2):S283-8. doi:
10.1007/s10545-010-9111-9
. [PMID: 20440648] - Alexandre F Solano, Guilhian Leipnitz, Giorgia M De Bortoli, Bianca Seminotti, Alexandre U Amaral, Carolina G Fernandes, Alexandra S Latini, Carlos S Dutra-Filho, Moacir Wajner. Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.
Free radical research.
2008 Aug; 42(8):707-15. doi:
10.1080/10715760802311179
. [PMID: 18661426] - M Kimura, S Yamaguchi. Screening for fatty acid beta oxidation disorders. Acylglycine analysis by electron impact ionization gas chromatography-mass spectrometry.
Journal of chromatography. B, Biomedical sciences and applications.
1999 Aug; 731(1):105-10. doi:
10.1016/s0378-4347(99)00208-x
. [PMID: 10491995] - I L Bykov, E Shigematsu. [Effect of l-carnitine on the expression of glycine conjugates in rats in experimental B2-hypovitaminosis].
Voprosy pitaniia.
1997; ?(6):9-11. doi:
NULL
. [PMID: 9541994] - M H Fries, P Rinaldo, E Schmidt-Sommerfeld, E Jurecki, S Packman. Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
The Journal of pediatrics.
1996 Sep; 129(3):449-52. doi:
10.1016/s0022-3476(96)70081-1
. [PMID: 8804338] - T Ito, K Kidouchi, N Sugiyama, M Kajita, T Chiba, T Niwa, Y Wada. Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
Journal of chromatography. B, Biomedical applications.
1995 Aug; 670(2):317-22. doi:
10.1016/0378-4347(95)00174-3
. [PMID: 8548022] - M Naglak, R Salvo, K Madsen, P Dembure, L Elsas. The treatment of isovaleric acidemia with glycine supplement.
Pediatric research.
1988 Jul; 24(1):9-13. doi:
10.1203/00006450-198807000-00004
. [PMID: 3137519] - D G Hine, A M Hack, S I Goodman, K Tanaka. Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
Pediatric research.
1986 Mar; 20(3):222-6. doi:
10.1203/00006450-198603000-00005
. [PMID: 3703611] - D G Hine, K Tanaka. The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
Pediatric research.
1984 Jun; 18(6):508-12. doi:
10.1203/00006450-198406000-00004
. [PMID: 6547525] - S Kølvraa, N Gregersen, E Christensen. In vivo studies on the metabolic derangement in a patient with D-glyceric acidaemia and hyperglycinaemia.
Journal of inherited metabolic disease.
1984; 7(2):49-52. doi:
10.1007/bf01805799
. [PMID: 6434823] - W G Wilson, S M Audenaert, E J Squillaro. Hyperammonaemia in a preterm infant with isovaleric acidaemia.
Journal of inherited metabolic disease.
1984; 7(2):71. doi:
10.1007/bf01805807
. [PMID: 6434830] - J A Bakkeren, R C Sengers, W Ruitenbeek, J M Trijbels, M L Houben, S P Van der Zeè. [Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Tijdschrift voor kindergeneeskunde.
1982 Oct; 50(5):153-9. doi:
NULL
. [PMID: 7157337] - Y Shigematsu, M Sudo, T Momoi, Y Inoue, Y Suzuki, J Kameyama. Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Pediatric research.
1982 Sep; 16(9):771-5. doi:
10.1203/00006450-198209000-00013
. [PMID: 7133811] - M Duran, L Bruinvis, D Ketting, S K Wadman, B C van Pelt, A M Batenburg-Plenter. Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
Journal of inherited metabolic disease.
1982; 5(2):125-7. doi:
10.1007/bf01800006
. [PMID: 6820423] - S Kølvraa, N Gregersen, N J Brandt. Excretion of short-chain N-acylglycines in the urine of a patient with D-glyceric acidemia.
Clinica chimica acta; international journal of clinical chemistry.
1980 Sep; 106(2):215-21. doi:
10.1016/0009-8981(80)90174-6
. [PMID: 7408214]